Ebstein's Anomaly

Ebstein’s anomaly is a rare congenital malformation characterized by apical displacement of the right atrioventricular ring with an development tricuspid valve and frequent presence other heart defects. According to our data, this defect was diagnosed in 2 cases more than 6 000 sectional studies: adult child. echocardiography rooms non-specialized multidisciplinary children's hospitals polyclinics, detected frequency 1:24.000–1:32.000 studies. Genetic environmental factors (viral infections, benzodiazepines, lithium) are indicated as probable causes. Clinical signs cyanosis, shortness breath, failure, cardiac arrhythmias. Morphologically there abnormalities valve, papillary muscles chordal apparatus, ventricular myocardial hypertrophy, thinning walls atrium atrialized part ventricle. Decisive for diagnosis ultrasound. Displacement revealed. The degree bias determines severity defect. amplitude movement increased. Its closure occurs later mitral. A 40 ms difference between mitral points diagnostically important sign anomaly. tactics doctor determined clinical picture